ICD-10-CM 2027
ICD-10 code for mitral stenosis
From the official ICD-10-CM alphabetic index entry “Stenosis, stenotic (cicatricial) › mitral (chronic) (inactive) (valve)”. Page updated September 29, 2026.
About coding mitral stenosis
The ICD-10-CM code for mitral stenosis is I05.0 (Rheumatic mitral stenosis). The official index lists 7 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on I05.0.
Within I05 (rheumatic mitral valve diseases), I05.0 is specifically for rheumatic mitral stenosis. Related codes cover rheumatic mitral insufficiency (I05.1), rheumatic mitral stenosis with insufficiency (I05.2), other rheumatic mitral valve diseases (I05.8) and rheumatic mitral valve disease, unspecified (I05.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific mitral stenosis codes (official index)
- with
- aortic valve disease I08.0 — Rheumatic disorders of both mitral and aortic valves
- incompetency, insufficiency or regurgitation I05.2 — Rheumatic mitral stenosis with insufficiency
- active or acute I01.1 — Acute rheumatic endocarditis
- with rheumatic or Sydenham's chorea I02.0 — Rheumatic chorea with heart involvement
- congenital Q23.2 — Congenital mitral stenosis
- specified cause, except rheumatic I34.2 — Nonrheumatic mitral (valve) stenosis
- syphilitic A52.03 — Syphilitic endocarditis
Common questions about mitral stenosis ICD-10 codes
What is the ICD-10 code for mitral stenosis?
- I05.0 — Rheumatic mitral stenosis. More specific codes apply when the documentation supports them: I08.0, I05.2, I01.1, I02.0 and others below.
What is the ICD-10 code for active or acute mitral stenosis?
- I01.1 — Acute rheumatic endocarditis.
What is the ICD-10 code for congenital mitral stenosis?
- Q23.2 — Congenital mitral stenosis.
What is the ICD-10 code for syphilitic mitral stenosis?
- A52.03 — Syphilitic endocarditis.
Is I05.0 billable?
- Yes. I05.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I05.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I05.0 as a principal diagnosis.
Is I05.0 a CC or MCC?
- No. I05.0 is neither a CC nor an MCC under MS-DRG v44.0.