ICD-10-CM 2027
ICD-10 code for Morquio syndrome mucopolysaccharidosis
From the official ICD-10-CM alphabetic index entry “Mucopolysaccharidosis › Morquio syndrome”. Page updated September 29, 2026.
About coding Morquio syndrome mucopolysaccharidosis
The ICD-10-CM code for Morquio syndrome mucopolysaccharidosis is E76.219 (Morquio mucopolysaccharidoses, unspecified). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on E76.219.
Within E76.21, choose E76.219 (unspecified) only when documentation doesn't support a more specific option: A mucopolysaccharidoses (E76.210) and B mucopolysaccharidoses (E76.211).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific Morquio syndrome mucopolysaccharidosis codes (official index)
Common questions about Morquio syndrome mucopolysaccharidosis ICD-10 codes
What is the ICD-10 code for Morquio syndrome mucopolysaccharidosis?
- E76.219 — Morquio mucopolysaccharidoses, unspecified. More specific codes apply when the documentation supports them: E76.210, E76.211, E76.210.
What is the ICD-10 code for a morquio syndrome mucopolysaccharidosis?
- E76.210 — Morquio A mucopolysaccharidoses.
What is the ICD-10 code for b morquio syndrome mucopolysaccharidosis?
- E76.211 — Morquio B mucopolysaccharidoses.
What is the ICD-10 code for classic morquio syndrome mucopolysaccharidosis?
- E76.210 — Morquio A mucopolysaccharidoses.
Is E76.219 billable?
- Yes. E76.219 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E76.219 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E76.219 as a principal diagnosis.
Is E76.219 a CC or MCC?
- E76.219 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.