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ICD-10-CM 2027

ICD-10 code for muscle deficiency

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Deficiency, deficient › muscle”. Page updated September 29, 2026.

About coding muscle deficiency

The official ICD-10-CM index doesn't give a single default code for muscle deficiency; the code depends on the details below.

More specific muscle deficiency codes (official index)

  • carnitine (palmityltransferase) E71.314 — Muscle carnitine palmitoyltransferase deficiency
  • phosphofructokinase E74.09 — Other glycogen storage disease

Common questions about muscle deficiency ICD-10 codes

What is the ICD-10 code for carnitine muscle deficiency?

E71.314 — Muscle carnitine palmitoyltransferase deficiency.

What is the ICD-10 code for phosphofructokinase muscle deficiency?

E74.09 — Other glycogen storage disease.