ICD-10-CM 2027
ICD-10 code for Nemaline myopathy
From the official ICD-10-CM alphabetic index entry “Myopathy › nemaline”. Page updated September 29, 2026.
About coding Nemaline myopathy
The ICD-10-CM code for Nemaline myopathy is G71.21 (Nemaline myopathy).
Within G71.2 (congenital myopathies), G71.21 is specifically for Nemaline myopathy. Related codes cover congenital myopathy, unspecified (G71.20), centronuclear myopathy (G71.22) and other congenital myopathy (G71.29).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Nemaline myopathy ICD-10 codes
What is the ICD-10 code for Nemaline myopathy?
- G71.21 — Nemaline myopathy.
Is G71.21 billable?
- Yes. G71.21 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G71.21 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G71.21 as a principal diagnosis.
Is G71.21 a CC or MCC?
- G71.21 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.