ICD-10-CM 2027
ICD-10 code for Nephronophthisis
From the official ICD-10-CM alphabetic index entry “Nephronophthisis”. Page updated September 29, 2026.
About coding Nephronophthisis
The ICD-10-CM code for Nephronophthisis is Q61.5 (Medullary cystic kidney).
Within Q61 (cystic kidney disease), Q61.5 is specifically for medullary cystic kidney. Related codes cover congenital renal cyst (Q61.0), polycystic kidney, infantile type (Q61.1), polycystic kidney, adult type (Q61.2), polycystic kidney, unspecified (Q61.3), renal dysplasia (Q61.4), other cystic kidney diseases (Q61.8) and unspecified (Q61.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 698 (Other Kidney and Urinary Tract Diagnoses with MCC, relative weight 1.6398), DRG 699 (Other Kidney and Urinary Tract Diagnoses with CC, relative weight 1.0003) and DRG 700 (Other Kidney and Urinary Tract Diagnoses without CC/MCC, relative weight 0.6741), in MDC 11 (Diseases and Disorders of the Kidney and Urinary Tract), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Nephronophthisis ICD-10 codes
What is the ICD-10 code for Nephronophthisis?
- Q61.5 — Medullary cystic kidney.
Is Q61.5 billable?
- Yes. Q61.5 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q61.5 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q61.5 as a principal diagnosis.
Is Q61.5 a CC or MCC?
- Q61.5 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.