ICD-10-CM 2027
ICD-10 code for Neuroretinopathy
From the official ICD-10-CM alphabetic index entry “Neuroretinopathy, hereditary optic”. Page updated September 29, 2026.
About coding Neuroretinopathy
The ICD-10-CM code for Neuroretinopathy is H47.22 (Hereditary optic atrophy).
Within H47.2 (optic atrophy), H47.22 is specifically for hereditary optic atrophy. Related codes cover unspecified optic atrophy (H47.20), primary optic atrophy (H47.21), glaucomatous optic atrophy (H47.23) and other optic atrophy (H47.29).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 123 (Neurological Eye Disorders, relative weight 0.822), in MDC 02 (Diseases and Disorders of the Eye), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Neuroretinopathy ICD-10 codes
What is the ICD-10 code for Neuroretinopathy?
- H47.22 — Hereditary optic atrophy.
Is H47.22 billable?
- Yes. H47.22 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can H47.22 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict H47.22 as a principal diagnosis.
Is H47.22 a CC or MCC?
- No. H47.22 is neither a CC nor an MCC under MS-DRG v44.0.