ICD-10-CM 2027
ICD-10 code for oculocutaneous albinism
From the official ICD-10-CM alphabetic index entry “Albinism, albino › oculocutaneous”. Page updated September 29, 2026.
About coding oculocutaneous albinism
The ICD-10-CM code for oculocutaneous albinism is E70.329 (Oculocutaneous albinism, unspecified). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on E70.329.
Within E70.32, choose E70.329 (unspecified) only when documentation doesn't support a more specific option: Tyrosinase negative oculocutaneous albinism (E70.320), Tyrosinase positive oculocutaneous albinism (E70.321) and other oculocutaneous albinism (E70.328).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific oculocutaneous albinism codes (official index)
Common questions about oculocutaneous albinism ICD-10 codes
What is the ICD-10 code for oculocutaneous albinism?
- E70.329 — Oculocutaneous albinism, unspecified. More specific codes apply when the documentation supports them: E70.328, E70.320, E70.321.
What is the ICD-10 code for other specified oculocutaneous albinism?
- E70.328 — Other oculocutaneous albinism.
What is the ICD-10 code for tyrosinase negative oculocutaneous albinism?
- E70.320 — Tyrosinase negative oculocutaneous albinism.
What is the ICD-10 code for tyrosinase positive oculocutaneous albinism?
- E70.321 — Tyrosinase positive oculocutaneous albinism.
Is E70.329 billable?
- Yes. E70.329 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E70.329 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E70.329 as a principal diagnosis.
Is E70.329 a CC or MCC?
- E70.329 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.