ICD-10-CM 2027
ICD-10 code for Opitz' disease
From the official ICD-10-CM alphabetic index entry “Opitz' disease”. Page updated September 29, 2026.
About coding Opitz' disease
The ICD-10-CM code for Opitz' disease is D73.2 (Chronic congestive splenomegaly).
Within D73 (diseases of spleen), D73.2 is specifically for chronic congestive splenomegaly. Related codes cover Hyposplenism (D73.0), Hypersplenism (D73.1), abscess of spleen (D73.3), cyst of spleen (D73.4), infarction of spleen (D73.5), other diseases of spleen (D73.8) and disease of spleen, unspecified (D73.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 814 (Reticuloendothelial and Immunity Disorders with MCC, relative weight 2.0729), DRG 815 (Reticuloendothelial and Immunity Disorders with CC, relative weight 1.0444) and DRG 816 (Reticuloendothelial and Immunity Disorders without CC/MCC, relative weight 0.7381), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Opitz' disease ICD-10 codes
What is the ICD-10 code for Opitz' disease?
- D73.2 — Chronic congestive splenomegaly.
Is D73.2 billable?
- Yes. D73.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D73.2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D73.2 as a principal diagnosis.
Is D73.2 a CC or MCC?
- No. D73.2 is neither a CC nor an MCC under MS-DRG v44.0.