ICD-10-CM 2027
ICD-10 code for optic nerve neuroma
From the official ICD-10-CM alphabetic index entry “Neuroma › optic (nerve)”. Page updated September 29, 2026.
About coding optic nerve neuroma
The ICD-10-CM code for optic nerve neuroma is D33.3 (Benign neoplasm of cranial nerves).
Within D33 (benign neoplasm of brain and other parts of central nervous system), D33.3 is specifically for benign neoplasm of cranial nerves. Related codes cover brain, supratentorial (D33.0), brain, infratentorial (D33.1), brain, unspecified (D33.2), spinal cord (D33.4), other specified parts of central nervous system (D33.7) and central nervous system, unspecified (D33.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 054 (Nervous System Neoplasms with MCC, relative weight 1.5194) and DRG 055 (Nervous System Neoplasms without MCC, relative weight 1.0296), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about optic nerve neuroma ICD-10 codes
What is the ICD-10 code for optic nerve neuroma?
- D33.3 — Benign neoplasm of cranial nerves.
Is D33.3 billable?
- Yes. D33.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D33.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D33.3 as a principal diagnosis.
Is D33.3 a CC or MCC?
- No. D33.3 is neither a CC nor an MCC under MS-DRG v44.0.