ICD-10-CM 2027
ICD-10 code for paracoccidioidomycosis
From the official ICD-10-CM alphabetic index entry “Paracoccidioidomycosis”. Page updated September 29, 2026.
About coding paracoccidioidomycosis
The ICD-10-CM code for paracoccidioidomycosis is B41.9 (Paracoccidioidomycosis, unspecified). The official index lists 6 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on B41.9.
Within B41, choose B41.9 (unspecified) only when documentation doesn't support a more specific option: pulmonary paracoccidioidomycosis (B41.0), disseminated paracoccidioidomycosis (B41.7) and other forms of paracoccidioidomycosis (B41.8).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 791 (Prematurity with Major Problems, relative weight 4.1075), DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), DRG 867 (Other Infectious and Parasitic Diseases Diagnoses with MCC, relative weight 2.1859), DRG 868 (Other Infectious and Parasitic Diseases Diagnoses with CC, relative weight 1.0235) and DRG 869 (Other Infectious and Parasitic Diseases Diagnoses without CC/MCC, relative weight 0.6787), in MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period) and MDC 18 (Infectious and Parasitic Diseases, Systemic or Unspecified Sites), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific paracoccidioidomycosis codes (official index)
- disseminated B41.7 — Disseminated paracoccidioidomycosis
- generalized B41.7 — Disseminated paracoccidioidomycosis
- mucocutaneous-lymphangitic B41.8 — Other forms of paracoccidioidomycosis
- pulmonary B41.0 — Pulmonary paracoccidioidomycosis
- specified NEC B41.8 — Other forms of paracoccidioidomycosis
- visceral B41.8 — Other forms of paracoccidioidomycosis
Common questions about paracoccidioidomycosis ICD-10 codes
What is the ICD-10 code for paracoccidioidomycosis?
- B41.9 — Paracoccidioidomycosis, unspecified. More specific codes apply when the documentation supports them: B41.7, B41.7, B41.8, B41.0 and others below.
What is the ICD-10 code for disseminated paracoccidioidomycosis?
- B41.7 — Disseminated paracoccidioidomycosis.
What is the ICD-10 code for generalized paracoccidioidomycosis?
- B41.7 — Disseminated paracoccidioidomycosis.
What is the ICD-10 code for mucocutaneous-lymphangitic paracoccidioidomycosis?
- B41.8 — Other forms of paracoccidioidomycosis.
What is the ICD-10 code for pulmonary paracoccidioidomycosis?
- B41.0 — Pulmonary paracoccidioidomycosis.
What is the ICD-10 code for visceral paracoccidioidomycosis?
- B41.8 — Other forms of paracoccidioidomycosis.
Is B41.9 billable?
- Yes. B41.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can B41.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict B41.9 as a principal diagnosis.
Is B41.9 a CC or MCC?
- B41.9 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.