ICD-10-CM 2027
ICD-10 code for Paraganglioma
From the official ICD-10-CM alphabetic index entry “Paraganglioma”. Page updated September 29, 2026.
About coding Paraganglioma
The ICD-10-CM code for Paraganglioma is D44.7 (Neoplasm of uncertain behavior of aortic body and other paraganglia). The official index lists 26 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on D44.7.
Within D44, choose D44.7 (aortic body and other paraganglia) only when documentation doesn't support a more specific option: thyroid gland (D44.0), adrenal gland (D44.1), parathyroid gland (D44.2), pituitary gland (D44.3), craniopharyngeal duct (D44.4), pineal gland (D44.5), carotid body (D44.6) and unspecified endocrine gland (D44.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 054 (Nervous System Neoplasms with MCC, relative weight 1.5194) and DRG 055 (Nervous System Neoplasms without MCC, relative weight 1.0296), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific Paraganglioma codes (official index)
- adrenal D35.0 — Benign neoplasm of adrenal gland
- malignant C74.1 — Malignant neoplasm of medulla of adrenal gland
- aortic body D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- malignant C75.5 — Malignant neoplasm of aortic body and other paraganglia
- carotid body D44.6 — Neoplasm of uncertain behavior of carotid body
- malignant C75.4 — Malignant neoplasm of carotid body
- chromaffin
- malignant
- extra-adrenal D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- malignant C75.5 — Malignant neoplasm of aortic body and other paraganglia
- specified site
- unspecified site C75.5 — Malignant neoplasm of aortic body and other paraganglia
- specified site
- unspecified site D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- gangliocytic D13.2 — Benign neoplasm of duodenum
- specified site
- unspecified site D13.2 — Benign neoplasm of duodenum
- glomus jugulare D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- malignant C75.5 — Malignant neoplasm of aortic body and other paraganglia
- jugular D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- malignant C75.5 — Malignant neoplasm of aortic body and other paraganglia
- specified site
- unspecified site C75.5 — Malignant neoplasm of aortic body and other paraganglia
- nonchromaffin D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- malignant C75.5 — Malignant neoplasm of aortic body and other paraganglia
- specified site
- unspecified site C75.5 — Malignant neoplasm of aortic body and other paraganglia
- specified site
- unspecified site D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- parasympathetic D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- specified site
- unspecified site D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- specified site
- sympathetic D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- specified site
- unspecified site D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
- unspecified site D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia
Common questions about Paraganglioma ICD-10 codes
What is the ICD-10 code for Paraganglioma?
- D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia. More specific codes apply when the documentation supports them: D35.0, C74.1, D44.7, C75.5 and others below.
What is the ICD-10 code for adrenal paraganglioma?
- D35.0 — Benign neoplasm of adrenal gland (header code; choose a more specific subcode).
What is the ICD-10 code for aortic body paraganglioma?
- D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia.
What is the ICD-10 code for carotid body paraganglioma?
- D44.6 — Neoplasm of uncertain behavior of carotid body.
What is the ICD-10 code for extra-adrenal paraganglioma?
- D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia.
What is the ICD-10 code for gangliocytic paraganglioma?
- D13.2 — Benign neoplasm of duodenum.
What is the ICD-10 code for glomus jugulare paraganglioma?
- D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia.
Is D44.7 billable?
- Yes. D44.7 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D44.7 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D44.7 as a principal diagnosis.
Is D44.7 a CC or MCC?
- No. D44.7 is neither a CC nor an MCC under MS-DRG v44.0.