ICD-10-CM 2027
ICD-10 code for Paraneoplastic pemphigus
From the official ICD-10-CM alphabetic index entry “Pemphigus › paraneoplastic”. Page updated September 29, 2026.
About coding Paraneoplastic pemphigus
The ICD-10-CM code for Paraneoplastic pemphigus is L10.81 (Paraneoplastic pemphigus).
Within L10.8 (other pemphigus), L10.81 is specifically for Paraneoplastic pemphigus. Related codes cover other pemphigus (L10.89).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 595 (Major Skin Disorders with MCC, relative weight 2.0239) and DRG 596 (Major Skin Disorders without MCC, relative weight 1.1071), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Paraneoplastic pemphigus ICD-10 codes
What is the ICD-10 code for Paraneoplastic pemphigus?
- L10.81 — Paraneoplastic pemphigus.
Is L10.81 billable?
- Yes. L10.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L10.81 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L10.81 as a principal diagnosis.
Is L10.81 a CC or MCC?
- L10.81 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.