ICD-10-CM 2027
ICD-10 code for Phosphomannomutase deficiency
From the official ICD-10-CM alphabetic index entry “Deficiency, deficient › phosphomannomutase”. Page updated September 29, 2026.
About coding Phosphomannomutase deficiency
The ICD-10-CM code for Phosphomannomutase deficiency is E74.818 (Other disorders of glucose transport).
Within E74.81, choose E74.818 (Other disorders of glucose transport) only when documentation doesn't support a more specific option: glucose transporter protein type 1 deficiency (E74.810) and disorders of glucose transport, unspecified (E74.819).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Phosphomannomutase deficiency ICD-10 codes
What is the ICD-10 code for Phosphomannomutase deficiency?
- E74.818 — Other disorders of glucose transport.
Is E74.818 billable?
- Yes. E74.818 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E74.818 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E74.818 as a principal diagnosis.
Is E74.818 a CC or MCC?
- E74.818 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.