ICD-10-CM 2027
ICD-10 code for POTS
From the official ICD-10-CM alphabetic index entry “POTS (postural orthostatic tachycardia syndrome)”. Page updated September 29, 2026.
About coding POTS
The ICD-10-CM code for POTS is G90.A (Postural orthostatic tachycardia syndrome [POTS]).
Within G90 (disorders of autonomic nervous system), G90.A is specifically for postural orthostatic tachycardia syndrome [POTS]. Related codes cover idiopathic peripheral autonomic neuropathy (G90.0), familial dysautonomia [Riley-Day] (G90.1), Horner's syndrome (G90.2), Multi-system degeneration of the autonomic nervous system (G90.3), autonomic dysreflexia (G90.4), complex regional pain syndrome I (CRPS I) (G90.5), other disorders of autonomic nervous system (G90.8), disorder of the autonomic nervous system, unspecified (G90.9) and 1 more.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239), DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 01 (Diseases and Disorders of the Nervous System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about POTS ICD-10 codes
What is the ICD-10 code for POTS?
- G90.A — Postural orthostatic tachycardia syndrome [POTS].
Is G90.A billable?
- Yes. G90.A is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G90.A be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G90.A as a principal diagnosis.
Is G90.A a CC or MCC?
- No. G90.A is neither a CC nor an MCC under MS-DRG v44.0.