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ICD-10-CM 2027

ICD-10 code for Pseudohypoparathyroidism

E20.1

Pseudohypoparathyroidism

✓ Billable / specific

From the official ICD-10-CM alphabetic index entry “Pseudohypoparathyroidism”. Page updated September 29, 2026.

About coding Pseudohypoparathyroidism

The ICD-10-CM code for Pseudohypoparathyroidism is E20.1 (Pseudohypoparathyroidism).

Within E20 (hypoparathyroidism), E20.1 is specifically for Pseudohypoparathyroidism. Related codes cover idiopathic hypoparathyroidism (E20.0), other hypoparathyroidism (E20.8) and unspecified (E20.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 640 (Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes with MCC, relative weight 1.3395) and DRG 641 (Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes without MCC, relative weight 0.7865), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

Common questions about Pseudohypoparathyroidism ICD-10 codes

What is the ICD-10 code for Pseudohypoparathyroidism?

E20.1 — Pseudohypoparathyroidism.

Is E20.1 billable?

Yes. E20.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can E20.1 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict E20.1 as a principal diagnosis.

Is E20.1 a CC or MCC?

No. E20.1 is neither a CC nor an MCC under MS-DRG v44.0.