ICD-10-CM 2027
ICD-10 code for retinal hereditary dystrophy
From the official ICD-10-CM alphabetic index entry “Dystrophy, dystrophia › retinal (hereditary)”. Page updated September 29, 2026.
About coding retinal hereditary dystrophy
The ICD-10-CM code for retinal hereditary dystrophy is H35.50 (Unspecified hereditary retinal dystrophy). The official index lists 6 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on H35.50.
Within H35.5, choose H35.50 (Unspecified hereditary retinal dystrophy) only when documentation doesn't support a more specific option: vitreoretinal dystrophy (H35.51), pigmentary retinal dystrophy (H35.52), other dystrophies primarily involving the sensory retina (H35.53) and dystrophies primarily involving the retinal pigment epithelium (H35.54).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 124 (Other Disorders of the Eye with MCC or Thrombolytic Agent, relative weight 1.2471) and DRG 125 (Other Disorders of the Eye without MCC, relative weight 0.7702), in MDC 02 (Diseases and Disorders of the Eye), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific retinal hereditary dystrophy codes (official index)
- in
- lipid storage disorders E75.6 — Lipid storage disorder, unspecified
- systemic lipidoses E75.6 — Lipid storage disorder, unspecified
- involving
- pigment epithelium H35.54 — Dystrophies primarily involving the retinal pigment epithelium
- sensory area H35.53 — Other dystrophies primarily involving the sensory retina
- pigmentary H35.52 — Pigmentary retinal dystrophy
- vitreoretinal H35.51 — Vitreoretinal dystrophy
Common questions about retinal hereditary dystrophy ICD-10 codes
What is the ICD-10 code for retinal hereditary dystrophy?
- H35.50 — Unspecified hereditary retinal dystrophy. More specific codes apply when the documentation supports them: E75.6, E75.6, H35.54, H35.53 and others below.
What is the ICD-10 code for pigmentary retinal hereditary dystrophy?
- H35.52 — Pigmentary retinal dystrophy.
What is the ICD-10 code for vitreoretinal retinal hereditary dystrophy?
- H35.51 — Vitreoretinal dystrophy.
Is H35.50 billable?
- Yes. H35.50 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can H35.50 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict H35.50 as a principal diagnosis.
Is H35.50 a CC or MCC?
- No. H35.50 is neither a CC nor an MCC under MS-DRG v44.0.