ICD-10-CM 2027
ICD-10 code for Ruvalcaba-Myhre-Smith syndrome
From the official ICD-10-CM alphabetic index entry “Ruvalcaba-Myhre-Smith syndrome”. Page updated September 29, 2026.
About coding Ruvalcaba-Myhre-Smith syndrome
The ICD-10-CM code for Ruvalcaba-Myhre-Smith syndrome is E71.440 (Ruvalcaba-Myhre-Smith syndrome).
Within E71.44 (other secondary carnitine deficiency), E71.440 is specifically for Ruvalcaba-Myhre-Smith syndrome. Related codes cover other secondary carnitine deficiency (E71.448).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Ruvalcaba-Myhre-Smith syndrome ICD-10 codes
What is the ICD-10 code for Ruvalcaba-Myhre-Smith syndrome?
- E71.440 — Ruvalcaba-Myhre-Smith syndrome.
Is E71.440 billable?
- Yes. E71.440 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.440 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.440 as a principal diagnosis.
Is E71.440 a CC or MCC?
- No. E71.440 is neither a CC nor an MCC under MS-DRG v44.0.