ICD-10-CM 2027
ICD-10 code for Schnitzler syndrome
From the official ICD-10-CM alphabetic index entry “Syndrome › Schnitzler”. Page updated September 29, 2026.
About coding Schnitzler syndrome
The ICD-10-CM code for Schnitzler syndrome is D47.2 (Monoclonal gammopathy).
Within D47 (other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue), D47.2 is specifically for monoclonal gammopathy. Related codes cover mast cell neoplasms of uncertain behavior (D47.0), chronic myeloproliferative disease (D47.1), essential (hemorrhagic) thrombocythemia (D47.3), Osteomyelofibrosis (D47.4), neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified (D47.9) and other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue (D47.Z).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 814 (Reticuloendothelial and Immunity Disorders with MCC, relative weight 2.0729), DRG 815 (Reticuloendothelial and Immunity Disorders with CC, relative weight 1.0444) and DRG 816 (Reticuloendothelial and Immunity Disorders without CC/MCC, relative weight 0.7381), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Schnitzler syndrome ICD-10 codes
What is the ICD-10 code for Schnitzler syndrome?
- D47.2 — Monoclonal gammopathy.
Is D47.2 billable?
- Yes. D47.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D47.2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D47.2 as a principal diagnosis.
Is D47.2 a CC or MCC?
- No. D47.2 is neither a CC nor an MCC under MS-DRG v44.0.