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ICD-10-CM 2027

ICD-10 code for septum agenesis

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Agenesis › septum”. Page updated September 29, 2026.

About coding septum agenesis

The official ICD-10-CM index doesn't give a single default code for septum agenesis; the code depends on the details below.

More specific septum agenesis codes (official index)

  • atrial Q21.19 — Other specified atrial septal defect
  • between aorta and pulmonary artery Q21.4 — Aortopulmonary septal defect
  • ventricular Q20.4 — Double inlet ventricle

Common questions about septum agenesis ICD-10 codes

What is the ICD-10 code for atrial septum agenesis?

Q21.19 — Other specified atrial septal defect.

What is the ICD-10 code for ventricular septum agenesis?

Q20.4 — Double inlet ventricle.