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ICD-10-CM 2027

ICD-10 code for Sézary disease

C84.1

Sezary disease

Header — needs a more specific code

From the official ICD-10-CM alphabetic index entry “Sézary disease”. Page updated October 2, 2026.

About coding Sézary disease

The ICD-10-CM code for Sézary disease is C84.1 (Sezary disease).

Within C84 (mature T/NK-cell lymphomas), C84.1 is specifically for Sezary disease. Related codes cover mycosis fungoides (C84.0), peripheral T-cell lymphoma, not elsewhere classified (C84.4), Anaplastic large cell lymphoma, ALK-positive (C84.6), Anaplastic large cell lymphoma, ALK-negative (C84.7), unspecified (C84.9), cutaneous T-cell lymphoma, unspecified (C84.A) and other mature T/NK-cell lymphomas (C84.Z).

To report this condition, pick the subcode that matches the documentation: C84.10 (unspecified site), C84.11 (lymph nodes of head, face, and neck), C84.12 (intrathoracic lymph nodes), C84.13 (intra-abdominal lymph nodes), C84.14 (lymph nodes of axilla and upper limb), C84.15 (lymph nodes of inguinal region and lower limb), C84.16 (intrapelvic lymph nodes), C84.17 (spleen) and 3 more.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Common questions about Sézary disease ICD-10 codes

What is the ICD-10 code for Sézary disease?

C84.1 — Sezary disease (a header code; report a more specific subcode).

Is C84.1 billable?

No. C84.1 is a header code. Report one of its more specific subcodes instead.