ICD-10-CM 2027
ICD-10 code for Shy-Drager syndrome
Multi-system degeneration of the autonomic nervous system
From the official ICD-10-CM alphabetic index entry “Shy-Drager syndrome”. Page updated September 29, 2026.
About coding Shy-Drager syndrome
The ICD-10-CM code for Shy-Drager syndrome is G90.3 (Multi-system degeneration of the autonomic nervous system).
Within G90 (disorders of autonomic nervous system), G90.3 is specifically for Multi-system degeneration of the autonomic nervous system. Related codes cover idiopathic peripheral autonomic neuropathy (G90.0), familial dysautonomia [Riley-Day] (G90.1), Horner's syndrome (G90.2), autonomic dysreflexia (G90.4), complex regional pain syndrome I (CRPS I) (G90.5), other disorders of autonomic nervous system (G90.8), disorder of the autonomic nervous system, unspecified (G90.9), postural orthostatic tachycardia syndrome [POTS] (G90.A) and 1 more.
Don't report G90.3 together with the conditions in its Excludes1 note: orthostatic hypotension NOS (I95.1).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for G90.3)
- orthostatic hypotension NOS (I95.1)
Common questions about Shy-Drager syndrome ICD-10 codes
What is the ICD-10 code for Shy-Drager syndrome?
- G90.3 — Multi-system degeneration of the autonomic nervous system.
Is G90.3 billable?
- Yes. G90.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G90.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G90.3 as a principal diagnosis.
Is G90.3 a CC or MCC?
- G90.3 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.