ICD-10-CM 2027
ICD-10 code for systemic scleroderma
From the official ICD-10-CM alphabetic index entry “Scleroderma, sclerodermia (acrosclerotic) (diffuse) (generalized) (progressive) (pulmonary) › systemic”. Page updated September 29, 2026.
About coding systemic scleroderma
The ICD-10-CM code for systemic scleroderma is M34.9 (Systemic sclerosis, unspecified).
Within M34, choose M34.9 (Systemic sclerosis, unspecified) only when documentation doesn't support a more specific option: progressive systemic sclerosis (M34.0), CR(E)ST syndrome (M34.1), systemic sclerosis induced by drug and chemical (M34.2) and other forms of systemic sclerosis (M34.8).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 545 (Connective Tissue Disorders with MCC, relative weight 2.3892), DRG 546 (Connective Tissue Disorders with CC, relative weight 1.1745) and DRG 547 (Connective Tissue Disorders without CC/MCC, relative weight 0.7526), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about systemic scleroderma ICD-10 codes
What is the ICD-10 code for systemic scleroderma?
- M34.9 — Systemic sclerosis, unspecified.
Is M34.9 billable?
- Yes. M34.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can M34.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict M34.9 as a principal diagnosis.
Is M34.9 a CC or MCC?
- No. M34.9 is neither a CC nor an MCC under MS-DRG v44.0.