ICD-10-CM 2027
ICD-10 code for uvula agenesis
From the official ICD-10-CM alphabetic index entry “Agenesis › uvula”. Page updated September 29, 2026.
About coding uvula agenesis
The ICD-10-CM code for uvula agenesis is Q38.5 (Congenital malformations of palate, not elsewhere classified).
Within Q38 (other congenital malformations of tongue, mouth and pharynx), Q38.5 is specifically for congenital malformations of palate, not elsewhere classified. Related codes cover congenital malformations of lips, not elsewhere classified (Q38.0), Ankyloglossia (Q38.1), Macroglossia (Q38.2), other congenital malformations of tongue (Q38.3), congenital malformations of salivary glands and ducts (Q38.4), other congenital malformations of mouth (Q38.6), congenital pharyngeal pouch (Q38.7) and other congenital malformations of pharynx (Q38.8).
Don't report Q38.5 together with the conditions in its Excludes1 note: cleft palate (Q35.-) and cleft palate with cleft lip (Q37.-).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Don't confuse with (Excludes1 for Q38.5)
Common questions about uvula agenesis ICD-10 codes
What is the ICD-10 code for uvula agenesis?
- Q38.5 — Congenital malformations of palate, not elsewhere classified.
Is Q38.5 billable?
- Yes. Q38.5 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q38.5 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q38.5 as a principal diagnosis.
Is Q38.5 a CC or MCC?
- No. Q38.5 is neither a CC nor an MCC under MS-DRG v44.0.