ICD-10-CM 2027
ICD-10 code for vulva agenesis
From the official ICD-10-CM alphabetic index entry “Agenesis › vulva”. Page updated September 29, 2026.
About coding vulva agenesis
The ICD-10-CM code for vulva agenesis is Q52.71 (Congenital absence of vulva).
Within Q52.7 (other and unspecified congenital malformations of vulva), Q52.71 is specifically for congenital absence of vulva. Related codes cover unspecified congenital malformations of vulva (Q52.70) and other congenital malformations of vulva (Q52.79).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 742 (Uterine and Adnexa Procedures for Non-Malignancy with CC/MCC, relative weight 1.8456), DRG 743 (Uterine and Adnexa Procedures for Non-Malignancy without CC/MCC, relative weight 1.2974), DRG 760 (Menstrual and Other Female Reproductive System Disorders with CC/MCC, relative weight 1.0129) and DRG 761 (Menstrual and Other Female Reproductive System Disorders without CC/MCC, relative weight 0.7041), in MDC 13 (Diseases and Disorders of the Female Reproductive System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about vulva agenesis ICD-10 codes
What is the ICD-10 code for vulva agenesis?
- Q52.71 — Congenital absence of vulva.
Is Q52.71 billable?
- Yes. Q52.71 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q52.71 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q52.71 as a principal diagnosis.
Is Q52.71 a CC or MCC?
- No. Q52.71 is neither a CC nor an MCC under MS-DRG v44.0.