ICD-10 code for Wegener's syndrome

The ICD-10-CM code for Wegener's syndrome is M31.30 (Wegener's granulomatosis without renal involvement). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on M31.30.

Within M31.3, choose M31.30 (without renal involvement) only when documentation doesn't support a more specific option: with renal involvement (M31.31).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 542 (Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with MCC, relative weight 1.7211), DRG 543 (Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with CC, relative weight 1.006) and DRG 544 (Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy without CC/MCC, relative weight 0.7406), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.