ICD-10-CM 2027
ICD-10 code for Werdnig-Hoffmann syndrome
Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
From the official ICD-10-CM alphabetic index entry “Werdnig-Hoffmann syndrome (muscular atrophy)”. Page updated September 29, 2026.
About coding Werdnig-Hoffmann syndrome
The ICD-10-CM code for Werdnig-Hoffmann syndrome is G12.0 (Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]).
Within G12 (spinal muscular atrophy and related syndromes), G12.0 is specifically for infantile spinal muscular atrophy, type I [Werdnig-Hoffman]. Related codes cover other inherited spinal muscular atrophy (G12.1), motor neuron disease (G12.2), other spinal muscular atrophies and related syndromes (G12.8) and spinal muscular atrophy, unspecified (G12.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 056 (Degenerative Nervous System Disorders with MCC, relative weight 2.2655) and DRG 057 (Degenerative Nervous System Disorders without MCC, relative weight 1.2838), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Werdnig-Hoffmann syndrome ICD-10 codes
What is the ICD-10 code for Werdnig-Hoffmann syndrome?
- G12.0 — Infantile spinal muscular atrophy, type I [Werdnig-Hoffman].
Is G12.0 billable?
- Yes. G12.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G12.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G12.0 as a principal diagnosis.
Is G12.0 a CC or MCC?
- G12.0 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.