ICD-10-CM 2027
ICD-10 code for Wilson's disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › Wilson's (hepatolenticular degeneration)”. Page updated September 29, 2026.
About coding Wilson's disease
The ICD-10-CM code for Wilson's disease is E83.01 (Wilson's disease).
Within E83.0 (disorders of copper metabolism), E83.01 is specifically for Wilson's disease. Related codes cover disorder of copper metabolism, unspecified (E83.00) and other disorders of copper metabolism (E83.09).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Wilson's disease ICD-10 codes
What is the ICD-10 code for Wilson's disease?
- E83.01 — Wilson's disease.
Is E83.01 billable?
- Yes. E83.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E83.01 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E83.01 as a principal diagnosis.
Is E83.01 a CC or MCC?
- No. E83.01 is neither a CC nor an MCC under MS-DRG v44.0.