ICD-10-CM 2027
ICD-10 code for Xanthogranuloma
From the official ICD-10-CM alphabetic index entry “Xanthogranuloma”. Page updated September 29, 2026.
About coding Xanthogranuloma
The ICD-10-CM code for Xanthogranuloma is D76.3 (Other histiocytosis syndromes).
Within D76, choose D76.3 (Other histiocytosis syndromes) only when documentation doesn't support a more specific option: Hemophagocytic lymphohistiocytosis (D76.1) and Hemophagocytic syndrome, infection-associated (D76.2).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 814 (Reticuloendothelial and Immunity Disorders with MCC, relative weight 2.0729), DRG 815 (Reticuloendothelial and Immunity Disorders with CC, relative weight 1.0444) and DRG 816 (Reticuloendothelial and Immunity Disorders without CC/MCC, relative weight 0.7381), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Xanthogranuloma ICD-10 codes
What is the ICD-10 code for Xanthogranuloma?
- D76.3 — Other histiocytosis syndromes.
Is D76.3 billable?
- Yes. D76.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D76.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D76.3 as a principal diagnosis.
Is D76.3 a CC or MCC?
- D76.3 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.