ICD-9-CM diagnosis code (retired)
270.1 — Phenylketonuria [PKU]
ICD-9-CM was replaced by ICD-10 on October 1, 2015. These are the ICD-10-CM equivalents from the CMS General Equivalence Mappings.
About ICD-9-CM 270.1
270.1 is an ICD-9-CM diagnosis code for phenylketonuria [PKU]. ICD-9-CM was retired for U.S. claims on October 1, 2015, when ICD-10-CM took over.
The CMS General Equivalence Mappings translate it to one ICD-10-CM code, E70.0 (Classical phenylketonuria). The match is approximate, so confirm it against the record.
ICD-10-CM equivalents
- E70.0Classical phenylketonuriaapproximate
Common questions about 270.1
What is the ICD-10 code for ICD-9 270.1?
- The GEMs map 270.1 to ICD-10-CM E70.0.
GEMs are a translation aid, not a substitute for coding from the record. The 2027 ICD-10 code set has changed since the last GEMs release in 2018. Page updated September 29, 2026.