ICD-9-CM diagnosis code (retired)
270.3 — Disturbances of branched-chain amino-acid metabolism
ICD-9-CM was replaced by ICD-10 on October 1, 2015. These are the ICD-10-CM equivalents from the CMS General Equivalence Mappings.
About ICD-9-CM 270.3
270.3 is an ICD-9-CM diagnosis code for disturbances of branched-chain amino-acid metabolism. ICD-9-CM was retired for U.S. claims on October 1, 2015, when ICD-10-CM took over.
The CMS General Equivalence Mappings translate it to 4 ICD-10-CM codes, such as E71.0 (Maple-syrup-urine disease), E71.120 (Methylmalonic acidemia) and E71.19 (Other disorders of branched-chain amino-acid metabolism). All of these are approximate matches, so review the record to pick the right one.
ICD-10-CM equivalents
Common questions about 270.3
GEMs are a translation aid, not a substitute for coding from the record. The 2027 ICD-10 code set has changed since the last GEMs release in 2018. Page updated September 29, 2026.