E00Congenital iodine-deficiency syndrome

E00 is the ICD-10-CM diagnosis code for congenital iodine-deficiency syndrome. It belongs to block E00-E07 (disorders of thyroid gland) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 4 subcodes must be used instead.

To report this condition, pick the subcode that matches the documentation: E00.0 (neurological type), E00.1 (myxedematous type), E00.2 (mixed type) and E00.9 (unspecified).

Don't report E00 together with the conditions in its Excludes1 note: subclinical iodine-deficiency hypothyroidism (E02).

Use an additional code (F70-F79) to identify associated intellectual disabilities..

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.