ICD-10-CM 2027 diagnosis code
H49.813Kearns-Sayre syndrome, bilateral
H49.813 is a valid, billable ICD-10-CM code for kearns-sayre syndrome, bilateral. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About H49.813
H49.813 is the ICD-10-CM diagnosis code for Kearns-Sayre syndrome, bilateral. It belongs to category H49 (paralytic strabismus), block H49-H52 (disorders of ocular muscles, binocular movement, accommodation and refraction) and chapter 7 (diseases of the eye and adnexa). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within H49.81 (Kearns-Sayre syndrome), H49.813 is specifically for Kearns-Sayre syndrome, bilateral. Related codes cover right eye (H49.811), left eye (H49.812) and unspecified eye (H49.819).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 277.87 (disorders of mitochondrial metabolism).
Notes that apply from higher levels
Instructions written at a parent level also apply to H49.813.
› From H49.81 Kearns-Sayre syndrome
- , if applicable, other manifestations, such as:
- heart block (I45.9)
› From H49 Paralytic strabismus
Broader instructions also apply from H49-H52 Disorders of ocular muscles, binocular movement, accommodation and refraction and Chapter 7: Diseases of the eye and adnexa.
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 10 · Endocrine, Nutritional and Metabolic Diseases and Disorders
ICD-9-CM equivalent
Converter →- 277.87Disorders of mitochondrial metabolismapproximate
From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about H49.813
Is H49.813 billable?
- Yes. H49.813 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can H49.813 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict H49.813 as a principal diagnosis.
Is H49.813 a CC or MCC?
- H49.813 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.
What DRG does H49.813 group to?
- H49.813 is used in the MS-DRG v44.0 logic for MS-DRG 642 (Inborn and Other Disorders of Metabolism). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for H49.813?
- The CMS General Equivalence Mappings map H49.813 to ICD-9-CM 277.87.