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ICD-10-CM 2027 diagnosis code

H57.01Argyll Robertson pupil, atypical

✓ Billable / specific

H57.01 is a valid, billable ICD-10-CM code for argyll robertson pupil, atypical. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About H57.01

H57.01 is the ICD-10-CM diagnosis code for Argyll Robertson pupil, atypical. It belongs to category H57 (other disorders of eye and adnexa), block H55-H57 (other disorders of eye and adnexa) and chapter 7 (diseases of the eye and adnexa). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within H57.0 (anomalies of pupillary function), H57.01 is specifically for Argyll Robertson pupil, atypical. Related codes cover unspecified anomaly of pupillary function (H57.00), Anisocoria (H57.02), Miosis (H57.03), Mydriasis (H57.04), Tonic pupil (H57.05) and other anomalies of pupillary function (H57.09).

Don't report H57.01 together with the conditions in its Excludes1 note: syphilitic Argyll Robertson pupil (A52.19).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 056 (Degenerative Nervous System Disorders with MCC, relative weight 2.2655) and DRG 057 (Degenerative Nervous System Disorders without MCC, relative weight 1.2838), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 379.45 (Argyll Robertson pupil, atypical).

Coding notes

Excludes1Not coded here — never report together with this code
  • syphilitic Argyll Robertson pupil (A52.19)

Notes that apply from higher levels

Instructions written at a parent level also apply to H57.01.

Broader instructions also apply from Chapter 7: Diseases of the eye and adnexa.

Alphabetic index entries

1 entries

Terms in the official ICD-10-CM index that lead to H57.01.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

ICD-9-CM equivalent

Converter →
  • 379.45Argyll Robertson pupil, atypicalexact

From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • No changes since FY2016.

Common questions about H57.01

Is H57.01 billable?

Yes. H57.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can H57.01 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict H57.01 as a principal diagnosis.

Is H57.01 a CC or MCC?

No. H57.01 is neither a CC nor an MCC under MS-DRG v44.0.

What DRG does H57.01 group to?

H57.01 is used in the MS-DRG v44.0 logic for MS-DRG 056 (Degenerative Nervous System Disorders with MCC) and MS-DRG 057 (Degenerative Nervous System Disorders without MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

What is the ICD-9 code for H57.01?

The CMS General Equivalence Mappings map H57.01 to ICD-9-CM 379.45.