J84.03Idiopathic pulmonary hemosiderosis

J84.03 is the ICD-10-CM diagnosis code for idiopathic pulmonary hemosiderosis. It belongs to category J84 (other interstitial pulmonary diseases), block J80-J84 (other respiratory diseases principally affecting the interstitium) and chapter 10 (diseases of the respiratory system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within J84.0 (alveolar and parieto-alveolar conditions), J84.03 is specifically for idiopathic pulmonary hemosiderosis. Related codes cover alveolar proteinosis (J84.01), pulmonary alveolar microlithiasis (J84.02) and other alveolar and parieto-alveolar conditions (J84.09).

Don't report J84.03 together with the conditions in its Excludes1 note: acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81).

Code first underlying disease, such as: disorders of iron metabolism (E83.1-).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 196 (Interstitial Lung Disease with MCC, relative weight 1.8336), DRG 197 (Interstitial Lung Disease with CC, relative weight 0.9492) and DRG 198 (Interstitial Lung Disease without CC/MCC, relative weight 0.7259), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is a manifestation code, so it describes the effect of an underlying disease and can't be the principal diagnosis. Code the underlying condition first.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 516.1 (idiopathic pulmonary hemosiderosis).