J84.843Alveolar capillary dysplasia with vein misalignment

J84.843 is the ICD-10-CM diagnosis code for alveolar capillary dysplasia with vein misalignment. It belongs to category J84 (other interstitial pulmonary diseases), block J80-J84 (other respiratory diseases principally affecting the interstitium) and chapter 10 (diseases of the respiratory system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within J84.84 (other interstitial lung diseases of childhood), J84.843 is specifically for alveolar capillary dysplasia with vein misalignment. Related codes cover neuroendocrine cell hyperplasia of infancy (J84.841), pulmonary interstitial glycogenosis (J84.842) and other interstitial lung diseases of childhood (J84.848).

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 196 (Interstitial Lung Disease with MCC, relative weight 1.8336), DRG 197 (Interstitial Lung Disease with CC, relative weight 0.9492), DRG 198 (Interstitial Lung Disease without CC/MCC, relative weight 0.7259), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 04 (Diseases and Disorders of the Respiratory System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 516.64 (alveolar capillary dysplasia with vein misalignment).