M34.81Systemic sclerosis with lung involvement

M34.81 is the ICD-10-CM diagnosis code for systemic sclerosis with lung involvement. It belongs to category M34 (systemic sclerosis [scleroderma]), block M30-M36 (systemic connective tissue disorders) and chapter 13 (diseases of the musculoskeletal system and connective tissue). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within M34.8 (other forms of systemic sclerosis), M34.81 is specifically for systemic sclerosis with lung involvement. Related codes cover systemic sclerosis with myopathy (M34.82), systemic sclerosis with polyneuropathy (M34.83) and other systemic sclerosis (M34.89).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 196 (Interstitial Lung Disease with MCC, relative weight 1.8336), DRG 197 (Interstitial Lung Disease with CC, relative weight 0.9492) and DRG 198 (Interstitial Lung Disease without CC/MCC, relative weight 0.7259), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 517.2 (lung involvement in systemic sclerosis) and 710.1 (systemic sclerosis).