Q33.0Congenital cystic lung

Q33.0 is the ICD-10-CM diagnosis code for congenital cystic lung. It belongs to category Q33 (congenital malformations of lung), block Q30-Q34 (congenital malformations of the respiratory system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q33 (congenital malformations of lung), Q33.0 is specifically for congenital cystic lung. Related codes cover accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), agenesis of lung (Q33.3), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6), other congenital malformations of lung (Q33.8) and congenital malformation of lung, unspecified (Q33.9).

Don't report Q33.0 together with the conditions in its Excludes1 note: cystic fibrosis (E84.0) and cystic lung disease, acquired or unspecified (J98.4).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 205 (Other Respiratory System Diagnoses with MCC, relative weight 1.8244) and DRG 206 (Other Respiratory System Diagnoses without MCC, relative weight 0.9257), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 748.4 (congenital cystic lung).