ICD-10-CM 2027 diagnosis code
Q42Congenital absence, atresia and stenosis of large intestine
Q42 is a header code, so it can't be reported by itself. Choose one of the 6 more specific codes beneath it.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About Q42
Q42 is the ICD-10-CM diagnosis code for congenital absence, atresia and stenosis of large intestine. It belongs to block Q38-Q45 (other congenital malformations of the digestive system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 6 subcodes must be used instead.
To report this condition, pick the subcode that matches the documentation: Q42.0 (fistula), Q42.1 (fistula), Q42.2 (fistula), Q42.3 (fistula), Q42.8 (intestine) and Q42.9 (part unspecified).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under Q42
- Q42.0Congenital absence, atresia and stenosis of rectum with fistulaBillable
- Q42.1Congenital absence, atresia and stenosis of rectum without fistulaBillable
- Q42.2Congenital absence, atresia and stenosis of anus with fistulaBillable
- Q42.3Congenital absence, atresia and stenosis of anus without fistulaBillable
- Q42.8Congenital absence, atresia and stenosis of other parts of large intestineBillable
- Q42.9Congenital absence, atresia and stenosis of large intestine, part unspecifiedBillable
Coding notes
- congenital obstruction, occlusion and stricture of large intestine
Notes that apply from higher levels
Instructions written at a parent level also apply to Q42.
Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.
Codes whose notes reference Q42
- K56Excludes1
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about Q42
Is Q42 billable?
- No. Q42 is a header code. Report one of its more specific subcodes instead.