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ICD-10-CM 2027 diagnosis code

Q44.71Alagille syndrome

✓ Billable / specificPOA exemptCC — complication/comorbidity

Q44.71 is a valid, billable ICD-10-CM code for alagille syndrome. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Looking up by condition? See ICD-10 code for Alagille syndrome.

Code last changed in FY2024 (effective October 1, 2023). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q44.71

Q44.71 is the ICD-10-CM diagnosis code for Alagille syndrome. It belongs to category Q44 (congenital malformations of gallbladder, bile ducts and liver), block Q38-Q45 (other congenital malformations of the digestive system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q44.7 (other congenital malformations of liver), Q44.71 is specifically for Alagille syndrome. Related codes cover other congenital malformation of liver, unspecified (Q44.70) and other congenital malformations of liver (Q44.79).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 441 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with MCC, relative weight 1.8219), DRG 442 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with CC, relative weight 0.9602) and DRG 443 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis without CC/MCC, relative weight 0.6885), in MDC 07 (Diseases and Disorders of the Hepatobiliary System and Pancreas), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It was added in FY2024, effective October 1, 2023.

Coding notes

Applicable toConditions and synonyms classified to this code
  • Alagille-Watson syndrome

Notes that apply from higher levels

Instructions written at a parent level also apply to Q44.71.

› From Q44.7 Other congenital malformations of liver
Code also
  • , if applicable, associated malformations affecting other systems

Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Alphabetic index entries

2 entries

Terms in the official ICD-10-CM index that lead to Q44.71.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2024 (effective 10/1/2023): Added
  • No changes since FY2024.

Common questions about Q44.71

Is Q44.71 billable?

Yes. Q44.71 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q44.71 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q44.71 as a principal diagnosis.

Is Q44.71 a CC or MCC?

Q44.71 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does Q44.71 group to?

Q44.71 is used in the MS-DRG v44.0 logic for MS-DRG 441 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with MCC), MS-DRG 442 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with CC) and MS-DRG 443 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.