ICD-10-CM 2027 diagnosis code
Q78.3Progressive diaphyseal dysplasia
Q78.3 is a valid, billable ICD-10-CM code for progressive diaphyseal dysplasia. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.
Looking up by condition? See ICD-10 code for Engelmann syndrome, ICD-10 code for Camurati-Engelmann syndrome.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About Q78.3
Q78.3 is the ICD-10-CM diagnosis code for progressive diaphyseal dysplasia. It belongs to category Q78 (other osteochondrodysplasias), block Q65-Q79 (congenital malformations and deformations of the musculoskeletal system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within Q78 (other osteochondrodysplasias), Q78.3 is specifically for progressive diaphyseal dysplasia. Related codes cover Osteogenesis imperfecta (Q78.0), Polyostotic fibrous dysplasia (Q78.1), Osteopetrosis (Q78.2), Enchondromatosis (Q78.4), Metaphyseal dysplasia (Q78.5), multiple congenital exostoses (Q78.6), other specified osteochondrodysplasias (Q78.8) and osteochondrodysplasia, unspecified (Q78.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 756.56 (multiple epiphyseal dysplasia).
Coding notes
- Camurati-Engelmann syndrome
Notes that apply from higher levels
Instructions written at a parent level also apply to Q78.3.
› From Q78 Other osteochondrodysplasias
- congenital myotonic chondrodystrophy (G71.13)
Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.
Alphabetic index entries
4 entriesTerms in the official ICD-10-CM index that lead to Q78.3.
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 08 · Diseases and Disorders of the Musculoskeletal System and Connective Tissue
ICD-9-CM equivalent
Converter →- 756.56Multiple epiphyseal dysplasiaapproximate
From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about Q78.3
Is Q78.3 billable?
- Yes. Q78.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q78.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q78.3 as a principal diagnosis.
Is Q78.3 a CC or MCC?
- No. Q78.3 is neither a CC nor an MCC under MS-DRG v44.0.
What DRG does Q78.3 group to?
- Q78.3 is used in the MS-DRG v44.0 logic for MS-DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC), MS-DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC) and MS-DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for Q78.3?
- The CMS General Equivalence Mappings map Q78.3 to ICD-9-CM 756.56.