ICD-10-CM 2027
ICD-10 code for Adrenogenitalism
From the official ICD-10-CM alphabetic index entry “Adrenogenitalism, congenital”. Page updated September 29, 2026.
About coding Adrenogenitalism
The ICD-10-CM code for Adrenogenitalism is E25.0 (Congenital adrenogenital disorders associated with enzyme deficiency).
Within E25 (adrenogenital disorders), E25.0 is specifically for congenital adrenogenital disorders associated with enzyme deficiency. Related codes cover other adrenogenital disorders (E25.8) and adrenogenital disorder, unspecified (E25.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 643 (Endocrine Disorders with MCC, relative weight 1.6139), DRG 644 (Endocrine Disorders with CC, relative weight 1.0044) and DRG 645 (Endocrine Disorders without CC/MCC, relative weight 0.7459), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Adrenogenitalism ICD-10 codes
What is the ICD-10 code for Adrenogenitalism?
- E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency.
Is E25.0 billable?
- Yes. E25.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E25.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E25.0 as a principal diagnosis.
Is E25.0 a CC or MCC?
- No. E25.0 is neither a CC nor an MCC under MS-DRG v44.0.