ICD-10-CM 2027
ICD-10 code for Agyria
From the official ICD-10-CM alphabetic index entry “Agyria”. Page updated September 29, 2026.
About coding Agyria
The ICD-10-CM code for Agyria is Q04.3 (Other reduction deformities of brain).
Within Q04, choose Q04.3 (Other reduction deformities of brain) only when documentation doesn't support a more specific option: congenital malformations of corpus callosum (Q04.0), Arhinencephaly (Q04.1), holoprosencephaly (Q04.2), Septo-optic dysplasia of brain (Q04.4), Megalencephaly (Q04.5), congenital cerebral cysts (Q04.6), other specified congenital malformations of brain (Q04.8) and congenital malformation of brain, unspecified (Q04.9).
Don't report Q04.3 together with the conditions in its Excludes1 note: congenital malformations of corpus callosum (Q04.0).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for Q04.3)
- congenital malformations of corpus callosum (Q04.0)
Common questions about Agyria ICD-10 codes
What is the ICD-10 code for Agyria?
- Q04.3 — Other reduction deformities of brain.
Is Q04.3 billable?
- Yes. Q04.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q04.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q04.3 as a principal diagnosis.
Is Q04.3 a CC or MCC?
- Q04.3 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.