ICD-10-CM 2027 diagnosis code
Q04Other congenital malformations of brain
Q04 is a header code, so it can't be reported by itself. Choose one of the 9 more specific codes beneath it.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About Q04
Q04 is the ICD-10-CM diagnosis code for other congenital malformations of brain. It belongs to block Q00-Q07 (congenital malformations of the nervous system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 9 subcodes must be used instead.
To report this condition, pick the subcode that matches the documentation: Q04.0 (callosum), Q04.1 (Arhinencephaly), Q04.2 (holoprosencephaly), Q04.3 (brain), Q04.4 (brain), Q04.5 (Megalencephaly), Q04.6 (cysts), Q04.8 (brain) and 1 more.
Don't report Q04 together with the conditions in its Excludes1 note: cyclopia (Q87.0) and macrocephaly (Q75.3).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under Q04
- Q04.0Congenital malformations of corpus callosumBillable
- Q04.1ArhinencephalyBillable
- Q04.2HoloprosencephalyBillable
- Q04.3Other reduction deformities of brainBillable
- Q04.4Septo-optic dysplasia of brainBillable
- Q04.5MegalencephalyBillable
- Q04.6Congenital cerebral cystsBillable
- Q04.8Other specified congenital malformations of brainBillable
- Q04.9Congenital malformation of brain, unspecifiedBillable
Coding notes
Notes that apply from higher levels
Instructions written at a parent level also apply to Q04.
Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about Q04
Is Q04 billable?
- No. Q04 is a header code. Report one of its more specific subcodes instead.