ICD-10-CM 2027
ICD-10 code for alveolar pulmonary proteinosis
From the official ICD-10-CM alphabetic index entry “Proteinosis › alveolar (pulmonary)”. Page updated September 29, 2026.
About coding alveolar pulmonary proteinosis
The ICD-10-CM code for alveolar pulmonary proteinosis is J84.01 (Alveolar proteinosis).
Within J84.0 (alveolar and parieto-alveolar conditions), J84.01 is specifically for alveolar proteinosis. Related codes cover pulmonary alveolar microlithiasis (J84.02), idiopathic pulmonary hemosiderosis (J84.03) and other alveolar and parieto-alveolar conditions (J84.09).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 196 (Interstitial Lung Disease with MCC, relative weight 1.8336), DRG 197 (Interstitial Lung Disease with CC, relative weight 0.9492) and DRG 198 (Interstitial Lung Disease without CC/MCC, relative weight 0.7259), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about alveolar pulmonary proteinosis ICD-10 codes
What is the ICD-10 code for alveolar pulmonary proteinosis?
- J84.01 — Alveolar proteinosis.
Is J84.01 billable?
- Yes. J84.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can J84.01 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict J84.01 as a principal diagnosis.
Is J84.01 a CC or MCC?
- J84.01 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.