ICD-10 code for Anoctaminopathy

The ICD-10-CM code for Anoctaminopathy is G71.035 (Limb girdle muscular dystrophy due to anoctamin-5 dysfunction).

Within G71.03 (limb girdle muscular dystrophies), G71.035 is specifically for limb girdle muscular dystrophy due to anoctamin-5 dysfunction. Related codes cover autosomal dominant limb girdle muscular dystrophy (G71.031), autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (G71.032), limb girdle muscular dystrophy due to dysferlin dysfunction (G71.033), limb girdle muscular dystrophy due to sarcoglycan dysfunction (G71.034), limb girdle muscular dystrophy due to fukutin related protein dysfunction (G71.036), other limb girdle muscular dystrophy (G71.038) and limb girdle muscular dystrophy, unspecified (G71.039).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.