G71.031Autosomal dominant limb girdle muscular dystrophy

G71.031 is the ICD-10-CM diagnosis code for autosomal dominant limb girdle muscular dystrophy. It belongs to category G71 (primary disorders of muscles), block G70-G73 (diseases of myoneural junction and muscle) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within G71.03 (limb girdle muscular dystrophies), G71.031 is specifically for autosomal dominant limb girdle muscular dystrophy. Related codes cover autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (G71.032), limb girdle muscular dystrophy due to dysferlin dysfunction (G71.033), limb girdle muscular dystrophy due to sarcoglycan dysfunction (G71.034), limb girdle muscular dystrophy due to anoctamin-5 dysfunction (G71.035), limb girdle muscular dystrophy due to fukutin related protein dysfunction (G71.036), other limb girdle muscular dystrophy (G71.038) and limb girdle muscular dystrophy, unspecified (G71.039).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It was added in FY2023, effective October 1, 2022.