ICD-10-CM 2027
ICD-10 code for aorta deformity
Congenital malformation of aorta unspecified
From the official ICD-10-CM alphabetic index entry “Deformity › aorta (arch) (congenital)”. Page updated September 29, 2026.
About coding aorta deformity
The ICD-10-CM code for aorta deformity is Q25.40 (Congenital malformation of aorta unspecified). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q25.40.
Within Q25.4, choose Q25.40 (Congenital malformation of aorta unspecified) only when documentation doesn't support a more specific option: absence and aplasia of aorta (Q25.41), hypoplasia of aorta (Q25.42), congenital aneurysm of aorta (Q25.43), congenital dilation of aorta (Q25.44), Double aortic arch (Q25.45), Tortuous aortic arch (Q25.46), right aortic arch (Q25.47), anomalous origin of subclavian artery (Q25.48) and 1 more.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific aorta deformity codes (official index)
- acquired I77.89 — Other specified disorders of arteries and arterioles
Common questions about aorta deformity ICD-10 codes
What is the ICD-10 code for aorta deformity?
- Q25.40 — Congenital malformation of aorta unspecified. More specific codes apply when the documentation supports them: I77.89.
What is the ICD-10 code for acquired aorta deformity?
- I77.89 — Other specified disorders of arteries and arterioles.
Is Q25.40 billable?
- Yes. Q25.40 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q25.40 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q25.40 as a principal diagnosis.
Is Q25.40 a CC or MCC?
- Q25.40 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.