Q25.4Other congenital malformations of aorta

Q25.4 is the ICD-10-CM diagnosis code for other congenital malformations of aorta. It belongs to category Q25 (congenital malformations of great arteries), block Q20-Q28 (congenital malformations of the circulatory system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 10 subcodes must be used instead.

Within Q25, choose Q25.4 (Other congenital malformations of aorta) only when documentation doesn't support a more specific option: Patent ductus arteriosus (Q25.0), coarctation of aorta (Q25.1), atresia of aorta (Q25.2), Supravalvular aortic stenosis (Q25.3), atresia of pulmonary artery (Q25.5), stenosis of pulmonary artery (Q25.6), other congenital malformations of pulmonary artery (Q25.7), other congenital malformations of other great arteries (Q25.8) and 1 more.

To report this condition, pick the subcode that matches the documentation: Q25.40 (unspecified), Q25.41 (aorta), Q25.42 (aorta), Q25.43 (aorta), Q25.44 (aorta), Q25.45 (arch), Q25.46 (arch), Q25.47 (arch) and 2 more.

Don't report Q25.4 together with the conditions in its Excludes1 note: hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2017 (expanded into subcodes).