ICD-10-CM 2027
ICD-10 code for aorta malformation
Congenital malformation of aorta unspecified
From the official ICD-10-CM alphabetic index entry “Malformation (congenital) › aorta”. Page updated September 29, 2026.
About coding aorta malformation
The ICD-10-CM code for aorta malformation is Q25.40 (Congenital malformation of aorta unspecified). The official index lists 12 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q25.40.
Within Q25.4, choose Q25.40 (Congenital malformation of aorta unspecified) only when documentation doesn't support a more specific option: absence and aplasia of aorta (Q25.41), hypoplasia of aorta (Q25.42), congenital aneurysm of aorta (Q25.43), congenital dilation of aorta (Q25.44), Double aortic arch (Q25.45), Tortuous aortic arch (Q25.46), right aortic arch (Q25.47), anomalous origin of subclavian artery (Q25.48) and 1 more.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific aorta malformation codes (official index)
- absence Q25.41 — Absence and aplasia of aorta
- aneurysm, congenital Q25.43 — Congenital aneurysm of aorta
- aplasia Q25.41 — Absence and aplasia of aorta
- atresia Q25.29 — Other atresia of aorta
- aortic arch Q25.21 — Interruption of aortic arch
- coarctation (preductal) (postductal) Q25.1 — Coarctation of aorta
- dilatation, congenital Q25.44 — Congenital dilation of aorta
- hypoplasia Q25.42 — Hypoplasia of aorta
- patent ductus arteriosus Q25.0 — Patent ductus arteriosus
- specified type NEC Q25.49 — Other congenital malformations of aorta
- stenosis Q25.1 — Coarctation of aorta
- supravalvular Q25.3 — Supravalvular aortic stenosis
Common questions about aorta malformation ICD-10 codes
What is the ICD-10 code for aorta malformation?
- Q25.40 — Congenital malformation of aorta unspecified. More specific codes apply when the documentation supports them: Q25.41, Q25.43, Q25.41, Q25.29 and others below.
What is the ICD-10 code for absence aorta malformation?
- Q25.41 — Absence and aplasia of aorta.
What is the ICD-10 code for aplasia aorta malformation?
- Q25.41 — Absence and aplasia of aorta.
What is the ICD-10 code for atresia aorta malformation?
- Q25.29 — Other atresia of aorta.
What is the ICD-10 code for coarctation aorta malformation?
- Q25.1 — Coarctation of aorta.
What is the ICD-10 code for hypoplasia aorta malformation?
- Q25.42 — Hypoplasia of aorta.
What is the ICD-10 code for patent ductus arteriosus aorta malformation?
- Q25.0 — Patent ductus arteriosus.
Is Q25.40 billable?
- Yes. Q25.40 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q25.40 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q25.40 as a principal diagnosis.
Is Q25.40 a CC or MCC?
- Q25.40 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.