ICD-10 code for Arhinencephaly

The ICD-10-CM code for Arhinencephaly is Q04.1 (Arhinencephaly).

Within Q04 (other congenital malformations of brain), Q04.1 is specifically for Arhinencephaly. Related codes cover congenital malformations of corpus callosum (Q04.0), holoprosencephaly (Q04.2), other reduction deformities of brain (Q04.3), Septo-optic dysplasia of brain (Q04.4), Megalencephaly (Q04.5), congenital cerebral cysts (Q04.6), other specified congenital malformations of brain (Q04.8) and congenital malformation of brain, unspecified (Q04.9).

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239), DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 01 (Diseases and Disorders of the Nervous System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.